A Case Study of Partial Agenesis of the Corpus Callosum: Audiological Implications

Skinner, Leanne and Hickson, Louise (2002) A Case Study of Partial Agenesis of the Corpus Callosum: Audiological Implications. Australian Journal of Audiology, 24 1: 36-45. doi:10.1375/audi.24.1.36.31115


Author Skinner, Leanne
Hickson, Louise
Title A Case Study of Partial Agenesis of the Corpus Callosum: Audiological Implications
Journal name Australian Journal of Audiology
ISSN 0157-1532
1443-4873
Publication date 2002-05
DOI 10.1375/audi.24.1.36.31115
Volume 24
Issue 1
Start page 36
End page 45
Total pages 10
Editor Teresa Ching
Place of publication Australia
Publisher Australian Academic Press Pty. Ltd.
Collection year 2002
Language eng
Subject C1
321025 Rehabilitation and Therapy - Hearing and Speech
730111 Hearing, vision, speech and their disorders
Abstract This case study presents four and a half years of audiological observations, testing and aural habilitation of a female child with a partial agenesis of the corpus callosum (ACC). The ACC was diagnosed by MRI scan performed at 6 months of age to eliminate neurological causes for the developmental delay. This child was also born with a cleft palate and was diagnosed with Robinow Syndrome at 3 years and 3 months of age. The audiological results showed an improvement in hearing thresholds over the 4-year period. The child’s ophthalmologist also reported an improvement in visual skills over time. The most interesting aspect of the child’s hearing was the discrepancy between the monaural and the binaural results. That is, when assessed binaurally she often presented with a mild to moderate mixed loss and, when assessed monaurally, she showed a moderate to severe mixed loss for the right ear and a severe mixed loss for the left ear. Over time, the discrepancy between the monaural and binaural results changed. When assessed binaurally, the loss decreased to normal low frequency hearing sloping to a mild high frequency loss. When assessed monaurally, the most recent results showed a mild loss for the right ear and a moderate loss for the left ear. This discrepancy between binaural and monaural results was evident for both aided and unaided tests. For the most recent thresholds, the binaural results were consistent with the right monaural thresholds for the first time over the four and a half years. Parental reports of the child’s hearing were consistent with the binaural clinical results. This case indicates the need for audiologists to (1) carefully monitor the hearing of children with ACC, (2) obtain monaural and binaural hearing and aided thresholds results, and (3) compare these children’s functional abilities with the objective test results obtained. This case does question whether hearing aids are appropriate for children with ACC. If hearing aids are deemed to be appropriate, then hearing aids with compression characteristics should be considered.
Q-Index Code C1

 
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