Physiological and perceptual features of dysarthria in Moebius syndrome: Directions for treatment

Murdoch B.E., Johnson S.M. and Theodoros D.G. (1997) Physiological and perceptual features of dysarthria in Moebius syndrome: Directions for treatment. Pediatric Rehabilitation, 1 2: 83-97.

Author Murdoch B.E.
Johnson S.M.
Theodoros D.G.
Title Physiological and perceptual features of dysarthria in Moebius syndrome: Directions for treatment
Journal name Pediatric Rehabilitation   Check publisher's open access policy
ISSN 1363-8491
Publication date 1997
Sub-type Article (original research)
Volume 1
Issue 2
Start page 83
End page 97
Total pages 15
Subject 2735 Pediatrics, Perinatology, and Child Health
2742 Rehabilitation
Abstract The functioning of the major subsystems of the speech production apparatus of a 12 year old female with Moebius syndrome was investigated using a battery of perceptual and physiological instrumental measures. Perceptual tests administered included: The Assessment of Intelligibility of Dysarthric Speech; the Frenchay Dysarthria Assessment; and a perceptual analysis of a speech sample based on a reading of the Grandfather Passage. Instrumental procedures included: spirometric and kinematic analysis of speech breathing; electroglottographic and aerodynamic evaluation of laryngeal function; nasometric assessment of velopharyngeal function; and evaluation of lip and tongue function using a variety of strain-gauge and pressure transducers. Consistent with the pathophysiological basis of Moebius syndrome, the major dysfunctions of the speech production mechanism were found at the level of the articulatory valve. Somewhat unexpectedly, however, impaired function was also identified at the level of the velopharyngeal and laryngeal valves by both the perceptual and instrumental assessments and at the level of the respiratory system by the physiological analysis alone. The results are discussed with reference to the neurological basis and clinical features of Moebius syndrome. The implications of the findings for the treatment of congenital dysarthria associated with Moebius syndrome are also discussed. The advantage of instrumental analysis over perceptual assessments in defining treatment goals for children with congenital dysarthria is high-lighted.
Keyword Dysarthria
Moebius syndrome
Speech disorder
Q-Index Code C1
Q-Index Status Provisional Code
Institutional Status Unknown

Document type: Journal Article
Sub-type: Article (original research)
Collection: Scopus Import
 
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